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KMID : 0665420220370040363
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Korean Journal of Food Culture
2022 Volume.37 No. 4 p.363 ~ p.375
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A Study on the Dietary Behaviors and Nutritional Statuses of Children with Galactosemia in Korea
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Seo Hye-Ji
Jeong Ye-Seung
Kim Yu-Ri
Oh Ji-Eun
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Abstract
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Galactosemia is a rare, hereditary metabolic disorder caused by the accumulation of galactose and its metabolites in thebody due to a lack of enzymes that convert galactose to glucose. This study aimed to investigate the dietary behaviors andnutritional statuses of patients with galactosemia and to provide basic information on the development of nutritioneducation programs to improve quality of dietary life. A survey was conducted on 13 parents of (<11 years of age) childrenwith galactosemia and 26 parents of (<11 years of age) children without galactosemia. Mean body mass index was greaterfor school-age children with galactosemia (18.77 kg/m2) than for corresponding normal children (16.55 kg/m2).
Underweight and obesity rates of children with galactosemia were greater than those of children without galactosemia. Inaddition, children with galactosemia had a higher food neophobia rate and thus consumed less food. Normal childrenexhibited a greater range of food preferences than those with galactosemia, especially for milk and dairy products (p= .001)and fats and sweets (p= .04). Reliable food databases and appropriate dietary recommendations are required to ensure theproper growth of children with galactosemia.
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KEYWORD
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Galactosemia, rare metabolic disease, dietary behavior, nutritional status
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